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ICD-10-CM Diagnosis Codes

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4. Endocrine, nutritional and metabolic diseases (E00-E89)

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E70-E88 Metabolic disorders (E70-E88)

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E88 Other and unspecified metabolic disorders

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E88.4 Mitochondrial metabolism disorders

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E88.40   Mitochondrial metabolism disorder, unspecified
E88.41   MELAS syndrome
E88.42   MERRF syndrome
E88.43   Disorders of mitochondrial tRNA synthetases
E88.49   Other mitochondrial metabolism disorders
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