Hereditary acrodermatitis enteropathica   37702000

SNOMED CT code


SNOMED code37702000
nameHereditary acrodermatitis enteropathica
statusactive
date introduced2002-01-31
fully specified name(s)Hereditary acrodermatitis enteropathica (disorder)
synonyms
  • AE - Acrodermatitis enteropathica
  • Primary zinc malabsorption
  • Danbolt-Close syndrome
  • Acrodermatitis enteropathica
  • Hereditary acrodermatitis enteropathica
  • Primary zinc malabsorption syndrome
  • Brandt syndrome
  • Danbolt-Closs syndrome
  • Hereditary acrodermatitis enterohepatica
attributes - group2
Finding siteSkin structure of extremity   116370005
Associated morphologyPapular rash   70831001
OccurrenceChildhood   255398004
parents
  • Hereditary disorder of the integument   363185004
  • Disorder of zinc metabolism   46727001
  • Gianotti-Crosti syndrome   82721003
  • Autosomal recessive hereditary disorder   85995004
hierarchies
a selection of possible paths
SNOMED CT Concept   138875005
  Clinical finding   404684003
    Integumentary system finding   106077005
      Disorder of integument   128598002
        Hereditary disorder of the integument   363185004
          Hereditary acrodermatitis enteropathica   37702000

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Metabolic disease   75934005
        Disorder of mineral metabolism   45744005
          Disorder of trace mineral metabolism   15616006
            Disorder of zinc metabolism   46727001
              Hereditary acrodermatitis enteropathica   37702000

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Finding of limb structure   302293008
      Disorder of limb   128605003
        Gianotti-Crosti syndrome   82721003
          Hereditary acrodermatitis enteropathica   37702000

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Genetic disease   782964007
        Hereditary disease   32895009
          Autosomal hereditary disorder   1899006
            Autosomal recessive hereditary disorder   85995004
              Hereditary acrodermatitis enteropathica   37702000

ancestors
sorted most to least specific
cpt crosswalks

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