Familial benign pemphigus   79468000

SNOMED CT code


SNOMED code79468000
nameFamilial benign pemphigus
statusactive
date introduced2002-01-31
fully specified name(s)Familial benign pemphigus (disorder)
synonyms
  • Benign familial chronic pemphigus
  • Familial benign pemphigus
  • Hailey-Hailey disease
  • Familial benign chronic pemphigus
  • Hailey Hailey disease
attributes - group2
Associated morphologyAcantholysis   43327007
Finding siteSkin structure   39937001
attributes - group1
Associated morphologyBlister   339008
Finding siteSkin structure   39937001
attributes - group3
Clinical courseChronic   90734009
attributes - group4
Has interpretationAbnormal   263654008
InterpretsKeratinization   44138005
parents
hierarchies
a selection of possible paths
SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Genetic disease   782964007
        Hereditary disease   32895009
          Autosomal hereditary disorder   1899006
            Autosomal dominant hereditary disorder   11164009
              Familial benign pemphigus   79468000

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Degenerative disorder   362975008
        Degenerative skin disorder   396325007
          Acantholytic dermatosis   1251371002
            Familial benign pemphigus   79468000

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Chronic disease   27624003
        Chronic disease of skin   128236002
          Familial benign pemphigus   79468000

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Integumentary system finding   106077005
      Disorder of integument   128598002
        Disorder of keratinization   277905003
          Inherited disorder of keratinization   254214009
            Familial benign pemphigus   79468000

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Integumentary system finding   106077005
      Disorder of integument   128598002
        Injury of integument   125592002
          Blister of skin   823996003
            Familial benign pemphigus   79468000

ancestors
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