4A44.1 Aortic arch syndrome
International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2026-01
Arteritis, often granulomatous, predominantly affecting the aorta and/or its major branches. Onset usually in patients younger than 50.
postcoordination
Add Stem and/or Extension codes to form a cluster code which adds detail to the condition.
synonyms
- Aortic arch syndrome
- Martorell 2 syndrome
- Raeder-Harbitz syndrome
- Takayasu aortitis
- Takayasu arteritis
- Takayasu disease
- Takayasu syndrome
- aortic arch arteritis
- chronic subclavian-carotid obstruction syndrome
- idiopathic aortitis
- idiopathic medial aortopathy and arteriopathy
- nonspecific aortoarteritis
- obliterative aortitis
- obliterative brachiocephalic arteritis syndrome
- pulseless disease
- sclerosing aortitis and arteritis
- subclavian-carotid obstruction syndrome
- young female aortic arch arteritis syndrome
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