4A60.0 Familial Mediterranean fever

International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2026-01

FMF is an autoinflammatory disease associated with mutations in pyrin resulting in enhanced IL1 beta production. This results in clinical attacks of inflammation in the form of fever and serositis in the form of peritoneal, pleural or synovial inflammation along with increased acute phase reactants.

synonyms

• Familial Mediterranean fever
• Armenian disease
• FMF - [familial mediterranean fever]
• Hereditary amyloid nephropathy
• Periodic disease
• Riemann periodic disease
• Siegal Cattan Mamou disease
• familial non-neuropathic amyloidosis
• familial recurrent polyserositis
• paroxysmal polyserositis
• periodic familial peritonitis
• periodic familial polyserositis
• periodic fever
• periodic polyserositis
• Familial Mediterranean fever with amyloidosis

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