LA8A.6 Congenital subpulmonary stenosis

International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2024-01

A congenital cardiovascular malformation associated with narrowing within the outflow tract supporting the pulmonary valve. Additional information: subvalvar (infundibular) pulmonary stenosis is a narrowing of the outflow tract of the ventricle immediately below the pulmonic valve. This term should preferably be used in the setting of abnormal ventriculo-arterial connections, such as double outlet ventricle. Although subvalvar pulmonary stenosis is a type of right ventricular outflow tract obstruction if the ventriculo-arterial connections are normal, in this setting 'Congenital right ventricular outflow tract obstruction' should be used. Subvalvar pulmonary stenosis is also a type of left ventricular outflow tract obstruction in the setting of discordant ventriculo-arterial connections; this term should be used when the obstruction is only apparent immediately below the pulmonary valve, otherwise the term 'Congenital left ventricular outflow tract obstruction' should be used

exclusions

• Double chambered right ventricle  (LA88.1)

synonyms

• Congenital subpulmonary stenosis
• infundibular pulmonary stenosis

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