DB93.21 Idiopathic copper-associated cirrhosis

International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2024-01

Idiopathic copper-associated cirrhosis is a rare copper-overload liver disease characterised by a rapidly progressive liver cirrhosis from the first few years of life leading to hepatic insufficiency and harbouring a specific pathological aspect: pericellular fibrosis, inflammatory infiltration, hepatocyte necrosis, absence of steatosis, poor regeneration and histochemical copper staining.

postcoordination

synonyms

• Idiopathic copper-associated cirrhosis
• Non-Wilsonian hepatic copper toxicosis of infancy and childhood
• Tyrolean infantile cirrhosis
• Idiopathic copper toxicosis
• Indian childhood cirrhosis

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