CB05.3 Interstitial lung diseases associated with metabolic diseases International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2024-01 Interstitial lung diseases associated with metabolic diseases refers to a group of lung diseases affecting the interstitium (the tissue and space around the air sacs of the lungs). This diagnosis is associated with a large class of genetic diseases involving disorders of metabolism.
code elsewhere postcoordination Add Stem and/or Extension codes to form a cluster code which adds detail to the condition.
Has causing condition - a selection is required - multiple selections are allowed [select] 5C50 Inborn errors of amino acid or other organic acid metabolism – 5C50.0 Phenylketonuria – 5C50.1 Disorders of tyrosine metabolism – 5C50.2 Disorders of histidine metabolism – 5C50.3 Disorders of tryptophan metabolism – 5C50.4 Disorders of lysine or hydroxylysine metabolism – 5C50.5 Disorders of the gamma-glutamyl cycle – 5C50.6 Disorders of serine metabolism – 5C50.7 Disorders of glycine metabolism – 5C50.8 Disorders of proline or hydroxyproline metabolism – 5C50.9 Disorders of ornithine metabolism – 5C50.A Disorders of urea cycle metabolism – 5C50.B Disorders of methionine cycle or sulphur amino acid metabolism – 5C50.C Disorders of beta or omega amino acid metabolism – 5C50.D Disorders of branched-chain amino acid metabolism – 5C50.E Organic aciduria – 5C50.F Disorders of peptide metabolism – 5C50.G Trimethylaminuria – 5C50.Y Other specified inborn errors of amino acid or other organic acid metabolism – 5C50.Z Inborn errors of amino acid or other organic acid metabolism, unspecified –– 5C50.00 Classical phenylketonuria –– 5C50.01 Nonclassical phenylketonuria –– 5C50.02 Embryofetopathy due to maternal phenylketonuria –– 5C50.0Y Other specified phenylketonuria –– 5C50.0Z Phenylketonuria, unspecified –– 5C50.10 Alkaptonuria –– 5C50.11 Tyrosinaemia type 1 –– 5C50.12 Tyrosinaemia type 2 –– 5C50.1Y Other specified disorders of tyrosine metabolism –– 5C50.1Z Disorders of tyrosine metabolism, unspecified –– 5C50.20 Histidinaemia –– 5C50.21 Urocanic aciduria –– 5C50.2Y Other specified disorders of histidine metabolism –– 5C50.2Z Disorders of histidine metabolism, unspecified –– 5C50.70 Glycine encephalopathy –– 5C50.71 Sarcosinaemia –– 5C50.7Y Other specified disorders of glycine metabolism –– 5C50.7Z Disorders of glycine metabolism, unspecified –– 5C50.A0 Argininosuccinic aciduria –– 5C50.A1 Carbamoylphosphate synthetase deficiency –– 5C50.A2 Argininaemia –– 5C50.A3 Citrullinaemia –– 5C50.AY Other specified disorders of urea cycle metabolism –– 5C50.AZ Disorders of urea cycle metabolism, unspecified –– 5C50.D0 Maple-syrup-urine disease –– 5C50.DY Other specified disorders of branched-chain amino acid metabolism –– 5C50.DZ Disorders of branched-chain amino acid metabolism, unspecified –– 5C50.E0 Classical organic aciduria –– 5C50.E1 Cerebral organic aciduria –– 5C50.EY Other specified organic aciduria –– 5C50.EZ Organic aciduria, unspecified –– 5C50.F0 Prolidase deficiency –– 5C50.F1 Carnosinaemia –– 5C50.F2 Homocarnosinosis –– 5C50.FY Other specified disorders of peptide metabolism –– 5C50.FZ Disorders of peptide metabolism, unspecified 5C51 Inborn errors of carbohydrate metabolism – 5C51.0 Disorders of the pentose phosphate pathway – 5C51.1 Disorders of glycerol metabolism – 5C51.2 Disorders of glyoxylate metabolism – 5C51.3 Glycogen storage disease – 5C51.4 Disorders of galactose metabolism – 5C51.5 Disorders of fructose metabolism – 5C51.Y Other specified inborn errors of carbohydrate metabolism – 5C51.Z Inborn errors of carbohydrate metabolism, unspecified –– 5C51.20 Primary hyperoxaluria type 1 –– 5C51.2Y Other specified disorders of glyoxylate metabolism –– 5C51.2Z Disorders of glyoxylate metabolism, unspecified –– 5C51.40 Galactose-1-phosphate uridyltransferase deficiency –– 5C51.41 Galactokinase deficiency –– 5C51.42 Glucose or galactose intolerance of newborn –– 5C51.4Y Other specified disorders of galactose metabolism –– 5C51.4Z Disorders of galactose metabolism, unspecified –– 5C51.50 Hereditary fructose intolerance –– 5C51.5Y Other specified disorders of fructose metabolism –– 5C51.5Z Disorders of fructose metabolism, unspecified 5C52 Inborn errors of lipid metabolism – 5C52.0 Inborn errors of fatty acid oxidation or ketone body metabolism – 5C52.1 Inborn errors of sterol metabolism – 5C52.2 Neutral lipid storage disease – 5C52.Y Other specified inborn errors of lipid metabolism – 5C52.Z Inborn errors of lipid metabolism, unspecified –– 5C52.00 Disorders of carnitine transport or the carnitine cycle –– 5C52.01 Disorders of mitochondrial fatty acid oxidation –– 5C52.02 Disorders of ketone body metabolism –– 5C52.03 Sjögren-Larsson syndrome –– 5C52.0Y Other specified inborn errors of fatty acid oxidation or ketone body metabolism –– 5C52.0Z Inborn errors of fatty acid oxidation or ketone body metabolism, unspecified –– 5C52.10 Disorders of cholesterol synthesis –– 5C52.11 Bile acid synthesis defect with cholestasis –– 5C52.1Y Other specified inborn errors of sterol metabolism –– 5C52.1Z Inborn errors of sterol metabolism, unspecified 5C53 Inborn errors of energy metabolism – 5C53.0 Disorders of pyruvate metabolism – 5C53.1 Disorders of the citric acid cycle – 5C53.2 Disorders of mitochondrial oxidative phosphorylation – 5C53.3 Disorders of mitochondrial membrane transport – 5C53.4 Disorders of creatine metabolism – 5C53.Y Other specified inborn errors of energy metabolism – 5C53.Z Inborn errors of energy metabolism, unspecified –– 5C53.00 Pyruvate kinase deficiency –– 5C53.01 Lactate dehydrogenase deficiency –– 5C53.02 Pyruvate dehydrogenase complex deficiency –– 5C53.03 Pyruvate carboxylase deficiency –– 5C53.0Y Other specified disorders of pyruvate metabolism –– 5C53.0Z Disorders of pyruvate metabolism, unspecified –– 5C53.20 Mitochondrial DNA depletion syndromes –– 5C53.21 Multiple mitochondrial DNA deletion syndromes –– 5C53.22 Coenzyme Q10 deficiency –– 5C53.23 Mitochondrial protein translation defects –– 5C53.24 Leigh syndrome –– 5C53.25 Isolated ATP synthase deficiency –– 5C53.2Y Other specified disorders of mitochondrial oxidative phosphorylation –– 5C53.2Z Disorders of mitochondrial oxidative phosphorylation, unspecified –– 5C53.30 Mitochondrial substrate carrier disorders –– 5C53.31 Mitochondrial protein import disorders –– 5C53.3Y Other specified disorders of mitochondrial membrane transport –– 5C53.3Z Disorders of mitochondrial membrane transport, unspecified 5C54 Inborn errors of glycosylation or other specified protein modification – 5C54.0 Disorders of protein N-glycosylation – 5C54.1 Disorders of protein O-glycosylation – 5C54.2 Disorders of multiple glycosylation or other pathways – 5C54.Y Other specified congenital disorders of glycosylation and protein modification – 5C54.Z Congenital disorders of glycosylation and protein modification, unspecified 5C55 Inborn errors of purine, pyrimidine or nucleotide metabolism – 5C55.0 Disorders of purine metabolism – 5C55.1 Disorders of pyrimidine metabolism – 5C55.2 Disorders of nucleotide metabolism – 5C55.Y Other specified inborn errors of purine, pyrimidine or nucleotide metabolism – 5C55.Z Inborn errors of purine, pyrimidine or nucleotide metabolism, unspecified –– 5C55.00 Xanthinuria –– 5C55.01 Lesch-Nyhan syndrome –– 5C55.0Y Other specified disorders of purine metabolism –– 5C55.0Z Disorders of purine metabolism, unspecified 5C56 Lysosomal diseases – 5C56.0 Sphingolipidosis – 5C56.1 Neuronal ceroid lipofuscinosis – 5C56.2 Glycoproteinosis – 5C56.3 Mucopolysaccharidosis – 5C56.4 Disorders of sialic acid metabolism – 5C56.Y Other specified lysosomal diseases – 5C56.Z Lysosomal diseases, unspecified –– 5C56.00 Gangliosidosis –– 5C56.01 Fabry disease –– 5C56.02 Metachromatic leukodystrophy –– 5C56.0Y Other specified sphingolipidosis –– 5C56.0Z Sphingolipidosis, unspecified –– 5C56.20 Mucolipidosis –– 5C56.21 Oligosaccharidosis –– 5C56.2Y Other specified glycoproteinosis –– 5C56.2Z Glycoproteinosis, unspecified –– 5C56.30 Mucopolysaccharidosis type 1 –– 5C56.31 Mucopolysaccharidosis type 2 –– 5C56.32 Mucopolysaccharidosis type 4 –– 5C56.33 Mucopolysaccharidosis type 6 –– 5C56.3Y Other specified mucopolysaccharidosis –– 5C56.3Z Mucopolysaccharidosis, unspecified 5C57 Peroxisomal diseases – 5C57.0 Disorders of peroxisome biogenesis – 5C57.1 Disorders of peroxisomal alpha-, beta- or omega-oxidation – 5C57.Y Other specified peroxisomal diseases – 5C57.Z Peroxisomal diseases, unspecified 5C58 Inborn errors of porphyrin or heme metabolism – 5C58.0 Disorders of bilirubin metabolism or excretion – 5C58.1 Porphyrias – 5C58.Y Other specified inborn errors of porphyrin or heme metabolism – 5C58.Z Inborn errors of porphyrin or heme metabolism, unspecified –– 5C58.00 Crigler-Najjar syndrome –– 5C58.01 Gilbert syndrome –– 5C58.02 Dubin-Johnson syndrome –– 5C58.03 Progressive familial intrahepatic cholestasis –– 5C58.04 Benign recurrent intrahepatic cholestasis –– 5C58.0Y Other specified disorders of bilirubin metabolism or excretion –– 5C58.0Z Disorders of bilirubin metabolism or excretion, unspecified –– 5C58.10 Porphyria cutanea tarda –– 5C58.12 Erythropoietic porphyrias –– 5C58.13 Variegate porphyria –– 5C58.1Y Other specified porphyrias –– 5C58.1Z Porphyrias, unspecified 5C59 Inborn errors of neurotransmitter metabolism – 5C59.0 Disorders of biogenic amine metabolism – 5C59.1 Disorders of gamma aminobutyric acid metabolism – 5C59.2 Disorders of pyridoxine metabolism – 5C59.Y Other specified inborn errors of neurotransmitter metabolism – 5C59.Z Inborn errors of neurotransmitter metabolism, unspecified –– 5C59.00 Disorders of catecholamine synthesis –– 5C59.01 Disorders of pterin metabolism –– 5C59.0Y Other specified disorders of biogenic amine metabolism –– 5C59.0Z Disorders of biogenic amine metabolism, unspecified 5C5A Alpha-1-antitrypsin deficiency 5C5Y Other specified inborn errors of metabolism 5C5Z Inborn errors of metabolism, unspecified 5C60 Disorders of amino acid absorption or transport – 5C60.0 Oculocerebrorenal syndrome – 5C60.1 Cystinosis – 5C60.2 Cystinuria – 5C60.Y Other specified disorders of amino acid absorption or transport – 5C60.Z Disorders of amino acid absorption or transport, unspecified 5C61 Disorders of carbohydrate absorption or transport – 5C61.0 Glucose-galactose malabsorption – 5C61.1 Maltase-glucoamylase deficiency – 5C61.2 Congenital sucrase-isomaltase deficiency – 5C61.3 Alpha, alpha trehalase deficiency – 5C61.4 Acquired monosaccharide malabsorption – 5C61.5 Disorders of facilitated glucose transport – 5C61.6 Lactose intolerance – 5C61.Y Other specified disorders of carbohydrate absorption or transport – 5C61.Z Disorders of carbohydrate absorption or transport, unspecified –– 5C61.40 Fructose malabsorption –– 5C61.4Y Other specified acquired monosaccharide malabsorption –– 5C61.4Z Acquired monosaccharide malabsorption, unspecified –– 5C61.60 Primary lactase deficiency –– 5C61.61 Congenital lactase deficiency –– 5C61.62 Secondary lactase deficiency –– 5C61.6Z Lactose intolerance, unspecified 5C62 Disorders of lipid absorption or transport 5C63 Disorders of vitamin or non-protein cofactor absorption or transport – 5C63.0 Disorders of cobalamin metabolism or transport – 5C63.1 Disorders of folate metabolism or transport – 5C63.2 Disorders of vitamin D metabolism or transport – 5C63.Y Other specified disorders of vitamin or non-protein cofactor absorption or transport – 5C63.Z Disorders of vitamin or non-protein cofactor absorption or transport, unspecified –– 5C63.20 Hypocalcaemic vitamin D dependent rickets –– 5C63.21 Hypocalcaemic vitamin D resistant rickets –– 5C63.22 Hypophosphataemic rickets –– 5C63.2Y Other specified disorders of vitamin D metabolism or transport –– 5C63.2Z Disorders of vitamin D metabolism or transport, unspecified 5C64 Disorders of mineral absorption or transport – 5C64.0 Disorders of copper metabolism – 5C64.1 Disorders of iron metabolism – 5C64.2 Disorders of zinc metabolism – 5C64.3 Disorders of phosphorus metabolism or phosphatases – 5C64.4 Disorders of magnesium metabolism – 5C64.5 Disorders of calcium metabolism – 5C64.6 Disorders of sodium metabolism – 5C64.7 Disorders of chloride metabolism – 5C64.Y Disorders of other specified mineral absorption and transport – 5C64.Z Disorders of mineral absorption or transport, unspecified –– 5C64.00 Wilson disease –– 5C64.0Y Other specified disorders of copper metabolism –– 5C64.0Z Disorders of copper metabolism, unspecified –– 5C64.10 Iron overload diseases –– 5C64.1Y Other specified disorders of iron metabolism –– 5C64.1Z Disorders of iron metabolism, unspecified –– 5C64.20 Acrodermatitis enteropathica –– 5C64.21 Zinc deficiency syndromes –– 5C64.2Y Other specified disorders of zinc metabolism –– 5C64.2Z Disorders of zinc metabolism, unspecified –– 5C64.40 Hypermagnesaemia –– 5C64.41 Hypomagnesaemia –– 5C64.4Z Disorders of magnesium metabolism, unspecified 5C6Y Other specified disorders of metabolite absorption or transport 5C6Z Disorders of metabolite absorption or transport, unspecified 5C70 Volume depletion – 5C70.0 Dehydration – 5C70.1 Hypovolaemia – 5C70.Y Other specified volume depletion – 5C70.Z Volume depletion, unspecified 5C71 Hyperosmolality or hypernatraemia 5C72 Hypo-osmolality or hyponatraemia 5C73 Acidosis – 5C73.0 Acute respiratory acidosis – 5C73.1 Chronic respiratory acidosis – 5C73.2 Anion gap metabolic acidosis – 5C73.Y Other specified acidosis – 5C73.Z Acidosis, unspecified 5C74 Alkalosis 5C75 Mixed disorder of acid-base balance 5C76 Hyperkalaemia 5C77 Hypokalaemia 5C78 Fluid overload 5C7Y Other specified disorders of fluid, electrolyte or acid-base balance 5C7Z Disorders of fluid, electrolyte or acid-base balance, unspecified 5C80 Hyperlipoproteinaemia – 5C80.0 Hypercholesterolaemia – 5C80.1 Hypertriglyceridaemia – 5C80.2 Mixed hyperlipidaemia – 5C80.3 Hyperalphalipoproteinaemia – 5C80.Y Other specified hyperlipoproteinaemia – 5C80.Z Hyperlipoproteinaemia, unspecified –– 5C80.00 Primary hypercholesterolaemia –– 5C80.01 Secondary hypercholesterolaemia –– 5C80.0Z Hypercholesterolaemia, unspecified 5C81 Hypolipoproteinaemia – 5C81.0 Hypoalphalipoproteinaemia – 5C81.1 Hypobetalipoproteinaemia – 5C81.Y Other specified hypolipoproteinaemia – 5C81.Z Hypolipoproteinaemia, unspecified 5C8Y Other specified disorders of lipoprotein metabolism or lipidaemias 5C8Z Unspecified disorders of lipoprotein metabolism or lipidaemias 5C90 Metabolic or transporter liver disease 5C90.0 Liver diseases due to urea cycle defects 5C90.1 Liver diseases due to disorders of porphyrin or bilirubin metabolism or transport 5C90.2 Liver diseases due to disorders of amino acid metabolism 5C90.3 Liver disease due to disorders of lysosomal storage 5C90.4 Liver diseases due to mitochondrial disorders 5C90.5 Liver diseases due to disorders of mineral metabolism 5C90.Y Other specified metabolic or transporter liver disease 5C90.Z Metabolic or transporter liver disease, unspecified 5D00 Amyloidosis – 5D00.0 AL amyloidosis – 5D00.1 AA amyloidosis – 5D00.2 Hereditary amyloidosis – 5D00.3 Dialysis-associated amyloidosis – 5D00.Y Other specified amyloidosis – 5D00.Z Amyloidosis, unspecified –– 5D00.20 Hereditary ATTR amyloidosis –– 5D00.21 Non-neuropathic heredofamilial amyloidosis –– 5D00.2Y Other specified hereditary amyloidosis –– 5D00.2Z Hereditary amyloidosis, unspecified 5D01 Tumour lysis syndrome 5D0Y Other specified metabolic disorders 5D2Z Metabolic disorders, unspecified –– 5C56.0Y Other specified sphingolipidosis – 5C60.Y Other specified disorders of amino acid absorption or transport – EC23.20 Oculocutaneous albinism
synonyms Interstitial lung diseases associated with metabolic diseases Interstitial lung disease in Gaucher disease Interstitial lung disease in Niemann-Pick disease Interstitial lung disease in protein intolerance
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