4A01.01 Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2026-01
This refers to a nonfamilial type of primary immune deficiency disease characterised by a reduction in at least two serum immunoglobulin isotypes. Circulating B cells may be normal or low.
synonyms
- Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
- Hypogammaglobulinaemia NOS
- acquired agammaglobulinaemia NOS
- agammaglobulinaemia NOS
- agammaglobulinaemia antibody deficiency syndrome
- common variable agammaglobulinaemia
- hypogammaglobulinaemia antibody deficiency syndrome
- nonfamilial agammaglobulinaemia
- nonfamilial hypogammaglobulinaemia
- Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
- immunoglobulin-bearing b-lymphocytes agammaglobulinaemia
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