5C58.01 Gilbert syndrome
International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2026-01
Gilbert's syndrome is an inherited liver disorder characterised by jaundice due to unconjugated hyperbilirubinemia, resulting from a partial deficiency in hepatic bilirubin glucuronosyltransferase activity.
synonyms
- Gilbert syndrome
- Gilbert cholaemia
- Gilbert disease
- Gilbert--Lereboullet syndrome
- Hyperbilirubinaemia type 1
- Meulengracht icterus
- Meulengracht syndrome
- benign unconjugated bilirubinaemia syndrome
- cholaemia familiaris simplex
- chronic intermittent juvenile jaundice
- congenital familial cholaemia
- constitutional hepatic dysfunction
- constitutional hyperbilirubinaemia (in part)
- familial cholaemia
- familial nonhaemolytic bilirubinaemia
- familial nonhaemolytic jaundice
- hereditary nonhaemolytic bilirubinaemia
- hereditary nonhaemolytic jaundice
- icterus intermittens juvenilis
- idiopathic hyperbilirubinaemia (in part)
- idiopathic unconjugated hyperbilirubinaemia
- low-grade chronic hyperbilirubinaemia syndrome
- physiologic cholaemia
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