8C70.3 Facioscapulohumeral muscular dystrophy
International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2026-01
Facioscapulohumeral muscular dystrophy (FSHD) is an autosomal dominantly inherited muscle disease characterised by progressive muscle weakness with initial focal involvement of the facial, shoulder and arm muscles.
postcoordination
Add Stem and/or Extension codes to form a cluster code which adds detail to the condition.
synonyms
- Facioscapulohumeral muscular dystrophy
- FMD - [facioscapulohumeral muscular dystrophy]
- FSH - [facioscapulohumeral muscular dystrophy]
- FSHD - [facioscapulohumeral muscular dystrophy]
- Landouzy-Dejerine disease
- Landouzy-Déjerine atrophy
- Landouzy-Déjerine dystrophy or facioscapulohumeral atrophy
- Landouzy-Déjérine muscular dystrophy
- facioscapulohumeral atrophy
- facioscapulohumeral muscle dystrophy
- facioscapulohumeral myopathy
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