3A50.02 Haemoglobin H disease (– α/– – included)
International Classification of Diseases for Mortality and Morbidity Statistics, 11th Revision, v2026-01
Haemoglobin H (HbH) disease is a moderate to severe form of alpha-thalassemia characterised by pronounced microcytic hypochromic haemolytic anaemia.
synonyms
- Haemoglobin H disease (– α/– – included)
- HbH - [haemoglobin H] disease
- alpha - /- - or mutational forms of alpha-thalassaemia
- alpha thalassaemia intermedia
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