Enzymes (see also Inborn errors metabolism lysosomal)   LP31392-1

▸ 1,4-Alpha glucan branching enzyme   LP15278-2

▸ 3-ketoacyl-CoA thiolase   LP173656-2

▸ 3-Methylcrotonyl-CoA carboxylase   LP201748-3

▸ 5,10-Methylenetetrahydrofolate reductase   LP15306-1

▸ 5-Methyltetrahydrofolate homocysteine methyltransferase   LP15307-9

▸ 5'-Nucleotidase   LP15305-3

▸ 6-Phosphogluconate dehydrogenase   LP15308-7

▸ Acetylcholinesterase   LP15315-2

▸ Acetyl-CoA:glucosamine acetyltransferase   LP14461-5

▸ Acid phosphatase   LP15316-0

▸ Acyl CoA dehydrogenases   LP200316-0

▸ Adenine phosphoribosyltransferase   LP95516-8

▸ Adenosine deaminase   LP15323-6

▸ Adenosine monophosphate deaminase   LP15326-9

▸ Adenosine triphosphatase   LP15328-5

▸ Adenosyl homocysteine hydrolase   LP61812-1

▸ Adenylate kinase   LP15020-8

▸ Adenylosuccinate lyase   LP15329-3

▸ Alanine aminopeptidase   LP15332-7

▸ Alanine aminotransferase   LP15333-5

▸ Alcohol dehydrogenase   LP15338-4

▸ Aldolase   LP15021-6

▸ Alkaline phosphatase   LP15346-7

▸ Alkyl-dihydroxyacetonephosphate synthase   LP201754-1

▸ Alpha hydroxybutyrate dehydrogenase   LP15295-6

▸ Alpha-methylacyl CoA racemase   LP201758-2

▸ Alpha naphthylesterase   LP15367-3

▸ Amylase   LP15355-8

▸ Amylase in fluid   LP69218-3

▸ Angiotensin converting enzyme   LP15387-1

▸ Aspartate aminotransferase   LP15426-7

▸ Aspartylglucosaminidase   LP14017-5

▸ Beta fructofuranosidase   LP15434-1

▸ Beta galactosidase   LP14018-3

▸ Beta hydroxybutyrate dehydrogenase   LP15437-4

▸ Beta-ureidopropionase   LP201761-6

▸ Ureidopropionate   LP212177-2

▸ Bisphosphoglycerate mutase   LP157537-4

▸ Carbonate dehydratase   LP15473-9

▸ Carnitine acyltransferase   LP15475-4

▸ Carnitine acyltransferase I   LP61815-4

▸ Carnitine acyltransferase II   LP61816-2

▸ Carnitine palmitoyltransferase   LP70624-9

▸ Catalase   LP15478-8

▸ Cathepsin A   LP199573-9

▸ Cathepsin D   LP18007-2

▸ Cathepsin K   LP95081-3

▸ Cathepsin L   LP95082-1

▸ Cathepsin S   LP95083-9

▸ Chitotriosidase   LP34570-9

▸ Cholinesterase   LP14299-9

▸ Chymopapain   LP15503-3

▸ Chymotrypsin   LP14654-5

▸ Citrate synthase   LP33248-3

▸ Coenzyme Q cytochrome C reductase (Complex III)   LP182323-8

▸ Coproporphyrinogen oxidase   LP15507-4

▸ Creatine kinase   LP15510-8

▸ Creatine transport protein   LP199559-8

▸ Cytochrome B5 reductase   LP15524-9

▸ Cystinyl aminopeptidase   LP15522-3

▸ Cytochrome B reductase   LP15523-1

▸ Cytochrome C oxidase   LP15525-6

▸ Cytosol aminopeptidase   LP15526-4

▸ Diamine oxidase   LP101306-1

▸ Dihydrolipoamide acetyl transferase   LP15537-1

▸ Dihydrolipoamide dehydrogenase   LP15538-9

▸ Dihydropteridine reductase   LP15539-7

▸ Dihydroxyacetone phosphate acylcoa acyl transferase   LP14025-8

▸ Diphosphoglycerate mutase   LP15025-7

▸ Diphosphoglycerate phosphatase   LP61817-0

▸ Dopamine beta-hydroxylase   LP15544-7

▸ Elastase   LP18546-9

▸ Enolase   LP15026-5

▸ Enteropeptidase   LP15549-6

▸ Ferrochelatase   LP15569-4

▸ Fructokinase   LP15577-7

▸ Fumarase   LP15582-7

▸ Galactokinase   LP15585-0

▸ Galactose 1 phosphate uridyl transferase   LP14026-6

▸ Gamma glutamyl cysteine synthetase   LP15589-2

▸ Gamma glutamyl transferase   LP15590-0

▸ Glucose phosphate isomerase   LP15028-1

▸ Glucose-6-Phosphatase   LP15600-7

▸ Glucose-6-Phosphate dehydrogenase   LP15601-5

▸ Glutamate decarboxylase   LP230194-5

▸ Glutamate dehydrogenase   LP15606-4

▸ Glutaryl CoA dehydrogenase   LP15610-6

▸ Glutathione peroxidase   LP15611-4

▸ Glutathione reductase   LP15612-2

▸ Glutathione S-transferase   LP15613-0

▸ Glutathione synthase   LP15614-8

▸ Glyceraldehyde 3 phosphate dehydrogenase   LP15029-9

▸ Glycogen synthase   LP15621-3

▸ Guanine deaminase   LP15626-2

▸ Heparan-N-sulfatase   LP14028-2

▸ Hexokinase   LP15631-2

▸ Histidine ammonia lyase   LP15638-7

▸ Hydroxymethylglutaryl CoA lyase   LP15649-4

▸ Hypoxanthine phosphoribosyltransferase   LP15652-8

▸ Iduronate-2-Sulfatase   LP14029-0

▸ Isocitrate dehydrogenase   LP15681-7

▸ Isomaltase   LP28457-7

▸ Lactate dehydrogenase   LP15033-1

▸ L-dopa decarboxylase   LP33053-7

▸ Lactase   LP207986-3

▸ Lecithin cholesterol acyltransferase   LP15695-7

▸ Leukocyte esterase   LP15701-3

▸ L-iditol dehydrogenase   LP15685-8

▸ Lipoprotein associated phospholipase A2   LP35390-1

▸ Lipoprotein lipase   LP15707-0

▸ Lysolecithin acyltransferase   LP15717-9

▸ Lysozyme   LP14684-2

▸ Malate dehydrogenase   LP15720-3

▸ Mannose-6-phosphate isomerase   LP186037-0

▸ Matrix metallopeptidase 2   LP173633-1

▸ Matrix metallopeptidase 9   LP97945-7

▸ Methionine adenosyltransferase   LP15731-0

▸ Methylenetetrahydrofolate dehydrogenase NAD   LP15733-6

▸ Methylenetetrahydrofolate dehydrogenase NADP   LP15734-4

▸ Methylmalonyl CoA mutase   LP15736-9

▸ Mitochondrial respiratory chain enzymes   LP189602-8

▸ Mitochondrial respiratory chain enzyme analysis   LP189532-7

▸ Monoamine oxidase   LP18217-7

▸ Monophosphoglyceromutase   LP15037-2

▸ Myeloperoxidase   LP29281-0

▸ NADH cytochrome C reductase   LP33249-1

▸ NADH dehydrogenase   LP15742-7

▸ NADH:ubiquinone reductase   LP200493-7

▸ Ornithine carbamoyltransferase   LP15754-2

▸ Palatinase   LP18576-6

▸ Palmitoyl protein thioesterase   LP32455-5

▸ Paraoxonase-arylesterase 1 (PON1)   LP157503-6

▸ Phosphoenolpyruvate carboxykinase   LP15800-3

▸ Phosphofructokinase   LP15038-0

▸ Phosphoglucomutase   LP15804-5

▸ D-3-phosphoglycerate dehydrogenase   LP200136-2

▸ Phosphoglycerate kinase   LP15039-8

▸ Phosphoglyceromutase   LP15805-2

▸ Phosphomannomutase 1   LP199552-3

▸ Phosphomannomutase 2   LP186036-2

▸ Phosphoribosylpyrophosphate synthetase   LP61823-8

▸ Phosphorylase   LP36786-9

▸ Phosphorylase kinase   LP31797-1

▸ Phytanoyl CoA hydroxlase   LP203307-6

▸ Porphobilinogen deaminase   LP15810-2

▸ Porphobilinogen synthase   LP15811-0

▸ Proline dipeptidase   LP15819-3

▸ Propionyl CoA Carboxylase   LP15821-9

▸ Protein kinase   LP15830-0

▸ Protein phosphatase 3   LP95253-8

▸ Purine nucleoside phosphorylase   LP15841-7

▸ Pyrimidine-5'-Nucleotidase   LP15844-1

▸ Pyruvate carboxylase   LP15846-6

▸ Pyruvate dehydrogenase   LP18605-3

▸ Pyruvate kinase   LP15160-2

▸ Pyruvate oxidase   LP15849-0

▸ Renin   LP15273-3

▸ Ribonuclease   LP15854-0

▸ Streptomyces proteinase   LP15869-8

▸ Stromelysin-1   LP185750-9

▸ Succinate cytochrome C reductase   LP33250-9

▸ Succinate dehydrogenase   LP33247-5

▸ Succinate semialdehyde dehydrogenase   LP201790-5

▸ Sucrase   LP18580-8

▸ Sulfatidase   LP32730-1

▸ Sulfite oxidase   LP15876-3

▸ Superoxide dismutase   LP15877-1

▸ Terminal deoxyribonucleotidyl transferase   LP15880-5

▸ Thiopurine methyltransferase   LP19492-5

▸ Thymidine kinase   LP36807-3

▸ Thymidine phosphorylase   LP31740-1

▸ Transaldolase   LP172734-8

▸ Transketolase   LP15908-4

▸ Trehalase   LP15910-0

▸ Triacylglycerol lipase   LP14915-0

▸ Triokinase   LP15926-6

▸ Triosephosphate isomerase   LP15043-0

▸ Tripeptide aminopeptidase   LP32667-5

▸ Tripeptidyl peptidase I   LP157346-0

▸ Tryptase   LP17650-0

▸ Tyrosine aminotransferase   LP15934-0

▸ Coenzyme Q10   LP19264-8

▸ Coenzyme Q10.reduced   LP207811-3

▸ Uridine   LP99932-3

▸ Uridine monophosphate synthetase   LP201792-1

▸ Uridine diphosphate glucose-4-Epimerase   LP15936-5

▸ Uridyl transferase   LP15940-7

▸ Uroporphyrinogen decarboxylase   LP15945-6

▸ Uroporphyrinogen III synthase   LP15044-8