ICD-10-CM Diagnosis Codes

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4. Endocrine, nutritional and metabolic diseases (E00-E89)

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E70-E88 Metabolic disorders (E70-E88)

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E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

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E71.1 Other disorders of branched-chain amino-acid metabolism

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E71.11 Branched-chain organic acidurias

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E71.110   Isovaleric acidemia
E71.111   3-methylglutaconic aciduria
E71.118   Other branched-chain organic acidurias
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