ICD-10-CM Diagnosis Codes

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4. Endocrine, nutritional and metabolic diseases (E00-E89)

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E70-E88 Metabolic disorders (E70-E88)

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E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

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E71.3 Disorders of fatty-acid metabolism

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E71.31 Disorders of fatty-acid oxidation

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E71.310   Long chain/very long chain acyl CoA dehydrogenase deficiency
E71.311   Medium chain acyl CoA dehydrogenase deficiency
E71.312   Short chain acyl CoA dehydrogenase deficiency
E71.313   Glutaric aciduria type II
E71.314   Muscle carnitine palmitoyltransferase deficiency
E71.318   Other disorders of fatty-acid oxidation
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