AHA Coding Clinic® for ICD-10-CM and ICD-10-PCS - 2018 Issue 4; New/Revised ICD-10-CM Codes
Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and Leukoencephalopathy
Code I67.8, Other specified cerebrovascular diseases, has been expanded and a new sub-subcategory (I67.85) created for hereditary cerebrovascular diseases. Two new codes were created as follows: I67.850 Cerebral autosomal dominant arteriopathy with subcortical infarct and leukoencephalopathy I67.858 Other hereditary cerebrovascular disease Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL) is a cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy. It is an autosomal dominant genetic disorder caused by mutations in the Notch3 gene. CADASIL can cause strokes, brain lesions, and other impairments. Symptoms of CADASIL can be variable. Initial symptoms are migraine...
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Article Overview
This premium article covers a revision to an ICD-10-CM cerebrovascular disease category and introduces new hereditary cerebrovascular disease codes in the context of CADASIL. It is relevant to coders, clinical documentation specialists, and healthcare teams working with neurologic and genetic disease documentation. The article also gives general clinical background on symptoms, disease progression, and related diagnoses that are documented separately.
Why This Topic Matters
Accurate documentation and classification of hereditary cerebrovascular conditions can affect diagnosis coding, record clarity, and downstream reporting for neurologic care.
What You Will Learn
- What hereditary cerebrovascular disease coding changes were introduced
- How CADASIL is clinically characterized at a high level
- Which associated neurologic conditions are noted as separate diagnoses
- Why this disease category matters for documentation and coding workflows
Who Should Read This
- Medical coders
- Clinical documentation specialists
- Health information management professionals
- Neurology practices
- Genetics-related clinical staff
Codes Discussed
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