AHA Coding Clinic® for ICD-10-CM and ICD-10-PCS - 2020 Issue 4; New/Revised ICD-10-CM Codes
Dravet Syndrome
Two new codes have been created to identify Dravet syndrome, intractable, with status epilepticus (G40.833) and without status epilepticus (G40.834).Dravet syndrome is a rare genetic encephalopathy that presents in the first year of life. It was previously known as severe myoclonic epilepsy in infancy and represents approximately 7% of all severe epilepsies starting before the age of three years. During the first year of life, the condition appears as frequent febrile seizures. As the condition progresses, typically other types of seizures, including myoclonus and status epilepticus, occur. Around the age of two years, intellectual development begins...
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Article Overview
This article covers a coding update for Dravet syndrome and gives a short background on the disorder’s clinical presentation and progression. It is relevant for medical coders, clinical documentation staff, and clinicians who need to understand how the diagnosis is discussed in coding resources and why the topic matters for accurate record review and reporting. The article includes a concise description of the condition’s onset, typical developmental course, and the broader context behind the coding change.
Why This Topic Matters
Dravet syndrome is a rare condition with coding implications that may affect diagnosis documentation and data capture. This article helps readers recognize the topic and understand the general clinical context behind the update without relying on the premium content.
What You Will Learn
- What Dravet syndrome is in broad clinical terms
- Why the topic has a coding update associated with it
- How the condition is generally described over time in clinical documentation
- Which audience groups may need to pay attention to this diagnosis update
Who Should Read This
- Medical coders
- Clinical documentation specialists
- Billing staff
- Clinicians
- Coding auditors
Codes Discussed
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