AHA Coding Clinic® for ICD-10-CM and ICD-10-PCS - 2025 Issue 4; New/Revised ICD-10-CM Codes
Fontan Circulation
Subcategory, I27.84, Fontan-related circulation, was created to capture Fontan-related circulation and related complications. The new codes in this subcategory are as follows:I27.840 Fontan-associated liver disease [FALD] I27.841 Fontan-associated lymphatic dysfunction I27.848 Other Fontan-associated condition I27.849 Fontan-related circulation, unspecified The Fontan operation (Fontan circulation) is a reconstructive procedure that improves circulation in pediatric patients with single ventricle congenital heart disease, tricuspid atresia, hypoplastic left heart syndrome, and double outlet right ventricle. While there are 50,000 to 70,000 individuals in the United States today who have survived because of the Fontan procedure, the &ldquo...
Subscribe or sign in to view the full article.
Article Overview
This article is for coding and clinical documentation professionals who need to understand a newly created ICD-10-CM subcategory tied to Fontan-related circulation and its associated complications. It reviews the general clinical background of Fontan physiology, the major complication categories discussed in the source, and the context for the new diagnosis classification without reproducing coding instructions or detailed selection rules.
Why This Topic Matters
Fontan patients can develop complex, serious downstream complications, and accurate diagnosis reporting depends on recognizing the specific complication categories now represented in ICD-10-CM. This topic is relevant for coders, CDI teams, and clinicians documenting congenital heart disease follow-up and related manifestations.
What You Will Learn
- The clinical background of Fontan circulation and Fontan physiology
- Why a new ICD-10-CM subcategory was created for Fontan-related conditions
- The major complication categories associated with Fontan circulation
- How the article frames Fontan-associated liver and lymphatic complications in broad terms
Who Should Read This
- Medical coders
- Clinical documentation integrity specialists
- Healthcare auditors
- Clinicians documenting congenital heart disease follow-up
Codes Discussed
Subscribe or sign in to view the full article.


Quick, Current, Complete - www.findacode.com