Interstitial Lung Conditions

Effective October 1, 2011, category 516, Other alveolar and parietoalveolar pneumonopathy, has been expanded to create new codes for several different interstitial lung conditions. These conditions are described below. Idiopathic Interstitial Pneumonia Code 516.3 has been expanded and the title changed from “idiopathic fibrosing alveolitis” to “idiopathic interstitial pneumonia.” Idiopathic interstitial pneumonias are a group of scarring lung diseases with distinctive presentations, pathophysiology and clinical course. Seven new codes have been created at this subcategory for specific types of idiopathic interstitial pneumonia (516.31-516.37); as well...

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Note:  The following article synopsis was NOT provided by the AHA. It was created by Find-A-Code/innoviHealth.

Article Overview

This article explains ICD-9-CM changes effective October 1, 2011 for interstitial lung conditions within category 516 and related subcategories. It is useful for coders, CDI staff, and respiratory/medical records professionals who need to understand the scope of revised diagnostic groupings, newly created codes, and the broader clinical categories covered by the update. The discussion spans adult idiopathic interstitial pneumonias, lymphangioleiomyomatosis, adult pulmonary Langerhans cell histiocytosis, and interstitial lung diseases of childhood, along with related revision and exclusion language.

Why This Topic Matters

Accurate indexing of interstitial lung disorders depends on recognizing how the ICD-9-CM category was reorganized and which diagnoses were added, revised, or moved. This article helps users orient themselves to the affected code families and clinical groupings without needing to interpret the full coding bulletin first.

Article Sections

  1. Idiopathic Interstitial Pneumonia

    Covers the adult idiopathic interstitial pneumonia grouping and its related diagnostic subtypes. Also discusses the broader clinical context for this family of interstitial lung disorders.

  2. Lymphangioleiomyomatosis

    Summarizes the separately created category for this rare lung disease and its general clinical context. The section places the condition within the broader interstitial lung update.

  3. Adult Pulmonary Langerhans Cell Histiocytosis [PLCH]

    Describes the newly created adult pulmonary Langerhans cell histiocytosis category and its general clinical framing. The discussion distinguishes this entity from related pediatric histiocytic disorders.

  4. Childhood Interstitial Lung Disease

    Reviews the childhood interstitial lung disease subcategory and the pediatric conditions included within it. The section addresses the overall grouping and the reasons it differs from adult classifications.

What You Will Learn

  • How the interstitial lung disease category was reorganized in the 2011 ICD-9-CM update
  • Which broad clinical groups were separated into new or revised subcategories
  • How childhood interstitial lung disease is framed in relation to adult interstitial lung disease
  • What types of related revision, addition, and exclusion language accompany the update

Who Should Read This

  • Medical coders
  • Coding auditors
  • Clinical documentation improvement specialists
  • Respiratory department staff
  • Health information management professionals

Codes Discussed

  • ICD-9-CM: 516.3
  • ICD-9-CM: 516.30
  • ICD-9-CM: 516.31
  • ICD-9-CM: 516.32
  • ICD-9-CM: 516.33
  • ICD-9-CM: 516.34
  • ICD-9-CM: 516.35
  • ICD-9-CM: 516.36
  • ICD-9-CM: 516.37
  • ICD-9-CM: 516.4
  • ICD-9-CM: 516.5
  • ICD-9-CM: 516.61
  • ICD-9-CM: 516.62
  • ICD-9-CM: 516.63
  • ICD-9-CM: 516.64
  • ICD-9-CM: 516.69
  • ICD-9-CM: 516.8
  • ICD-9-CM: 136.3

Code Ranges Discussed

  • ICD-9-CM: 516.31-516.37

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