AHA Coding Clinic® for ICD-10-CM and ICD-10-PCS - 2025 Issue 4; New/Revised ICD-10-CM Codes
Kabuki Syndrome
Code Q89.81, Kabuki syndrome, has been specifically created to identify Kabuki syndrome (KS). KS is a rare genetic disorder characterized by distinctive facial features, growth delays, intellectual disability, and skeletal abnormalities. This syndrome affects multiple body systems, and the symptoms and severity can vary significantly among individuals. ...
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Article Overview
This short article provides a high-level introduction to Kabuki syndrome and identifies its dedicated diagnosis code in ICD-10-CM. It is relevant to coders, billers, clinicians, and revenue cycle staff who need a quick reference for recognizing the condition and understanding that the page is centered on a specific coded diagnosis.
Why This Topic Matters
Kabuki syndrome is uncommon and can involve multiple body systems, so accurate identification and documentation may be important for diagnosis reporting and record review. The article helps readers quickly determine whether they need the full premium content for more detail on this condition and its coding context.
What You Will Learn
- What Kabuki syndrome is at a general level
- That the article references a dedicated diagnosis code for the condition
- Why the condition may require attention across multiple body systems
- Who may benefit from reviewing the full article
Who Should Read This
- Medical coders
- Billing staff
- Clinical documentation specialists
- Health information management professionals
- Clinicians
Codes Discussed
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