AHA Coding Clinic® for ICD-9 - 2004 Issue 4; VOLUMES 1 AND 2 NEW/REVISED DIAGNOSIS CODES
Peroxisomal Disorders
Effective October 1, 2004, code 277.86, Peroxisomal disorders, has been created to uniquely identify peroxisomal disorders. Peroxisomal disorders are rare congenital diseases that are characterized by the absence of normal peroxisomes in the cells of the body. The most common is X-linked adrenoleukodystrophy with an incidence of 1 in 17,000. Others have an overall estimate of about 1 in 50,000. Peroxisomes contain enzymes that function as catalysts in metabolic processes. They are responsible for oxidation of fatty acids, biosynthesis of membrane phospholipids (plasmalogens), cholesterol and bile acids, conversion of amino acids into glucose, reduction of hydrogen...
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Article Overview
This article explains the addition of a new diagnosis code for peroxisomal disorders and provides background on the condition category, associated congenital metabolic disorders, and general clinical features. It is relevant to coding professionals, clinical documentation teams, and other healthcare staff who need to understand the scope of the diagnosis term and its coding context.
Why This Topic Matters
It helps readers recognize a newly established diagnosis category, understand the broader disorder group it represents, and note the stated effective date and exclusion reference.
What You Will Learn
- How the article frames peroxisomal disorders as a diagnosis category
- The clinical and congenital context associated with the disorder group
- The effective date and coding update referenced in the article
- The exclusion reference noted alongside the new diagnosis entry
Who Should Read This
- Medical coders
- Coding educators
- Clinical documentation specialists
- Healthcare compliance staff
- Revenue cycle professionals
Codes Discussed
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