AHA Coding Clinic® for ICD-10-CM and ICD-10-PCS - 2022 Issue 4; New/Revised ICD-10-CM Codes
Von Willebrand Disease
Code D68.0, Von Willebrand disease, was expanded and new codes created to specifically identify Von Willebrand disease (VWD) by type. VWD has been classified into six categories or subtypes, based on the differences in clinical features and therapeutic requirements as follows:D68.00, Von Willebrand disease, unspecified D68.01, Von Willebrand disease, type 1 D68.020, Von Willebrand disease, type 2A D68.021, Von Willebrand disease, type 2B D68.022, Von Willebrand disease, type 2M D68.023, Von Willebrand disease, type 2N D68.029, Von Willebrand disease, type 2, unspecified D68.03, Von Willebrand disease, type 3 D68.04...
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Article Overview
This article reviews Von Willebrand disease as a coding and classification topic, with emphasis on ICD-10-CM code assignment by disease type. It is intended for medical coders, compliance staff, and other revenue cycle professionals who need a high-level understanding of how the condition is organized in the code set and how documentation may reflect different disease subtypes and related bleeding disorders.
Why This Topic Matters
Accurate classification of Von Willebrand disease affects diagnosis coding, documentation integrity, and claims processing when providers document specific subtypes or related coagulation conditions.
Article Sections
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ICD-10-CM code expansion for Von Willebrand disease
This section introduces the updated ICD-10-CM classification for Von Willebrand disease and lists the subtype-based code structure.
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Overview of Von Willebrand disease and major types
This section describes the condition in general and summarizes the main clinical types discussed in the article.
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Type 1, type 2, and type 3 characteristics
This section outlines broad distinctions among the major disease types and their subtypes.
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Inheritance, symptoms, and acquired disease
This section discusses general disease patterns, common signs, and the distinction between inherited and acquired forms.
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Documentation scenario and coding question
This section presents a documentation scenario involving Von Willebrand disease and a related factor deficiency and frames a coding query about the diagnosis assignment.
What You Will Learn
- How Von Willebrand disease is organized into ICD-10-CM categories
- What broad clinical distinctions exist among the major disease types
- How documentation may mention related coagulation deficiencies alongside Von Willebrand disease
- What kind of coding issue arises when multiple related diagnoses are documented together
Who Should Read This
- Medical coders
- Coding auditors
- Compliance professionals
- Revenue cycle staff
- Clinical documentation improvement specialists
Codes Discussed
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