Hereditary pediatric Behçet-like disease   1187119002

SNOMED CT code


SNOMED code1187119002
nameHereditary pediatric Behçet-like disease
statusactive
date introduced2021-11-30
fully specified name(s)Hereditary pediatric Behçet-like disease (disorder)
synonyms
  • Behçet-like disease due to HA20
  • Hereditary paediatric Behçet-like disease
  • Hereditary pediatric Behçet-like disease
  • Behçet-like disease due to haploinsufficiency of A20
attributes - group3
Clinical courseRecurrent   255227004
attributes - group2
Finding siteImmune system structure   116003000
Associated morphologyInflammatory morphology   409774005
Pathological processAbnormal immune process   769247005
parents
hierarchies
a selection of possible paths
SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Genetic disease   782964007
        Hereditary disease   32895009
          Autosomal hereditary disorder   1899006
            Autosomal dominant hereditary disorder   11164009
              Hereditary pediatric Behçet-like disease   1187119002

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Systemic disease   56019007
        Haploinsufficiency of A20   1290916005
          Hereditary pediatric Behçet-like disease   1187119002

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Disorder of immune function   414029004
        Hereditary disorder of immune system   363138005
          Hereditary pediatric Behçet-like disease   1187119002

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Recurrent disease   58184002
        Hereditary pediatric Behçet-like disease   1187119002

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