Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome   1237349008

SNOMED CT code


SNOMED code1237349008
nameHydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome
statusactive
date introduced2022-09-30
fully specified name(s)Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome (disorder)
synonyms
  • Hydrops, lactic acidosis, sideroblastic anaemia, multisystemic failure syndrome
  • Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome
attributes - group1
OccurrenceFetal period   303112003
Associated morphologyHydrops   20741006
attributes - group2
OccurrenceCongenital   255399007
Associated morphologyMorphologically abnormal structure   49755003
Pathological processPathological developmental process   308490002
parents
hierarchies
a selection of possible paths
SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Metabolic disease   75934005
        Mitochondrial cytopathy   240096000
          Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome   1237349008

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Fetal finding   106112009
      Fetal disorder   70591005
        Metabolic disorder of fetus   363204006
          Fetal acidosis   240306004
            Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome   1237349008

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Edema   267038008
      Disorder characterized by edema   118654009
        Hydrops fetalis   276508000
          Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome   1237349008

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Finding of blood, lymphatics and immune system   299691001
      Disorder of cellular component of blood   414022008
        Anemia   271737000
          Sideroblastic anemia   41841004
            Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome   1237349008

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Fetal finding   106112009
      Fetal disorder   70591005
        Fetal anemia   462166006
          Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome   1237349008

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Developmental disorder   5294002
        Congenital malformation   276654001
          Congenital malformation syndrome   400038003
            Multiple system malformation syndrome   82354003
              Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome   1237349008

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Metabolic disease   75934005
        Disorder of acid-base balance   26436007
          Acidosis   51387008
            Metabolic acidosis   59455009
              Metabolic acidosis, increased anion gap (IAG)   25998009
                Metabolic acidosis, IAG, accumulation of organic acids   51294009
                  Lactic acidosis   91273001
                    Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome   1237349008

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