Retinal arterial macroaneurysm with supravalvular pulmonic stenosis   764452004

SNOMED CT code


SNOMED code764452004
nameRetinal arterial macroaneurysm with supravalvular pulmonic stenosis
statusactive
date introduced2018-07-31
fully specified name(s)Retinal arterial macroaneurysm with supravalvular pulmonic stenosis (disorder)
synonyms
  • FRAM - familial retinal arterial macroaneurysm
  • Retinal arterial macroaneurysm with supravalvular pulmonic stenosis
  • RAMSVPS - retinal arterial macroaneurysm with supravalvular pulmonic stenosis
  • Familial retinal arterial macroaneurysm
attributes - group3
Associated morphologyMacroaneurysm   784180002
Finding siteStructure of retinal artery   27988004
attributes - group2
Pathological processPathological developmental process   308490002
OccurrenceCongenital   255399007
Associated morphologyAneurysm   85659009
Finding siteStructure of retinal artery   27988004
attributes - group1
Pathological processPathological developmental process   308490002
Finding siteSuprapulmonic valve area structure   79142001
Associated morphologyStenosis   415582006
OccurrenceCongenital   255399007
parents
  • Familial disease   111941005
  • Retinal macroaneurysm   247124009
  • Cardiovascular system hereditary disorder   363005004
  • Developmental hereditary disorder   363070008
  • Hereditary disorder of the visual system   363343008
  • Congenital supravalvular pulmonary stenosis   52757001
  • Autosomal recessive hereditary disorder   85995004
  • Congenital retinal aneurysm   943003
hierarchies
a selection of possible paths
SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Familial disease   111941005
        Retinal arterial macroaneurysm with supravalvular pulmonic stenosis   764452004

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Finding of head and neck region   118254002
      Aneurysm of head and neck artery   301432000
        Retinal macroaneurysm   247124009
          Retinal arterial macroaneurysm with supravalvular pulmonic stenosis   764452004

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Cardiovascular finding   106063007
      Disorder of cardiovascular system   49601007
        Cardiovascular system hereditary disorder   363005004
          Retinal arterial macroaneurysm with supravalvular pulmonic stenosis   764452004

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Developmental disorder   5294002
        Developmental hereditary disorder   363070008
          Retinal arterial macroaneurysm with supravalvular pulmonic stenosis   764452004

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Eye / vision finding   118235002
      Visual system disorder   128127008
        Hereditary disorder of the visual system   363343008
          Retinal arterial macroaneurysm with supravalvular pulmonic stenosis   764452004

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Disorder of body system   362965005
        Disorder of mediastinum   49483002
          Pulmonary trunk abnormality   253620009
            Congenital abnormality of pulmonary trunk   448472004
              Congenital supravalvular pulmonary stenosis   52757001
                Retinal arterial macroaneurysm with supravalvular pulmonic stenosis   764452004

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Disease   64572001
      Genetic disease   782964007
        Hereditary disease   32895009
          Autosomal hereditary disorder   1899006
            Autosomal recessive hereditary disorder   85995004
              Retinal arterial macroaneurysm with supravalvular pulmonic stenosis   764452004

SNOMED CT Concept   138875005
  Clinical finding   404684003
    Finding of head and neck region   118254002
      Aneurysm of head and neck artery   301432000
        Congenital retinal aneurysm   943003
          Retinal arterial macroaneurysm with supravalvular pulmonic stenosis   764452004

ancestors
sorted most to least specific
cpt crosswalks

Rules-based maps relating CPT® codes to and from SNOMED CT® clinical concepts.  Forward and backward mapping allows for easy transition between code sets. Map-A-Code crosswalk tool easily crosswalks multiple codes between the code sets.

Access to this feature is available in the following products:
  • CPT® to SNOMED Crosswalks

demo
request yours today
subscribe
start today
newsletter
free subscription

Thank you for choosing Find-A-Code, please Sign In to remove ads.