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ICD-10-CM Diagnosis Codes

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4. Endocrine, nutritional and metabolic diseases (E00-E89)

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E70-E88 Metabolic disorders (E70-E88)

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E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

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E71.0   Maple-syrup-urine disease
E71.110E71.19   E71.1 Other disorders of branched-chain amino-acid metabolism
E71.2   Disorder of branched-chain amino-acid metabolism, unsp
E71.30E71.39   E71.3 Disorders of fatty-acid metabolism
E71.40E71.448   E71.4 Disorders of carnitine metabolism
E71.50E71.548   E71.5 Peroxisomal disorders
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