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ICD-10-CM Diagnosis Codes

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4. Endocrine, nutritional and metabolic diseases (E00-E89)

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E70-E88 Metabolic disorders (E70-E88)

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E72 Other disorders of amino-acid metabolism

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E72.2 Disorders of urea cycle metabolism

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E72.20   Disorder of urea cycle metabolism, unspecified
E72.21   Argininemia
E72.22   Arginosuccinic aciduria
E72.23   Citrullinemia
E72.29   Other disorders of urea cycle metabolism
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