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ICD-10-CM Diagnosis Codes

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4. Endocrine, nutritional and metabolic diseases (E00-E89)

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E70-E88 Metabolic disorders (E70-E88)

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E76 Disorders of glycosaminoglycan metabolism

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E76.01E76.03   E76.0 Mucopolysaccharidosis, type I
E76.1   Mucopolysaccharidosis, type II
E76.210E76.29   E76.2 Other mucopolysaccharidoses
E76.3   Mucopolysaccharidosis, unspecified
E76.8   Other disorders of glucosaminoglycan metabolism
E76.9   Glucosaminoglycan metabolism disorder, unspecified
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