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ICD-10-CM Diagnosis Codes

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17. Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)

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Q20-Q28 Congenital malformations of the circulatory system (Q20-Q28)

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Q26 Congenital malformations of great veins

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Q26.0   Congenital stenosis of vena cava
Q26.1   Persistent left superior vena cava
Q26.2   Total anomalous pulmonary venous connection
Q26.3   Partial anomalous pulmonary venous connection
Q26.4   Anomalous pulmonary venous connection, unspecified
Q26.5   Anomalous portal venous connection
Q26.6   Portal vein-hepatic artery fistula
Q26.8   Other congenital malformations of great veins
Q26.9   Congenital malformation of great vein, unspecified
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